DOI: 10.1210/me.2002-0055. Steroid Deficiency Syndromes in Mice with Targeted Disruption of Cyp11a1

Steroid Deficiency Syndromes in Mice with Targeted Disruption of Cyp11a1

10.1210/me.2002-0055

Crossref journal-article

The Endocrine Society

Molecular Endocrinology (80)

Bibliography

Hu, M.-C., Hsu, N.-C., El Hadj, N. B., Pai, C.-I., Chu, H.-P., Wang, C.-K. L., & Chung, B. (2002). Steroid Deficiency Syndromes in Mice with Targeted Disruption of Cyp11a1. Molecular Endocrinology, 16(8), 1943â1950.

Authors 7

Meng-Chun Hu (first)
Nai-Chi Hsu (additional)
Noomen Ben El Hadj (additional)
Chin-I Pai (additional)
Hsueh-Ping Chu (additional)
Chi-Kuang Leo Wang (additional)
Bon-chu Chung (additional)

References 24 Referenced 125

10.1016/S0039-128X(96)00156-0 / Steroids / Transcriptional regulation of the CYP11A1 and ferredoxin genes. by Chung B-c, Guo (1997)
10.1210/edrv-9-3-295 / Endocr Rev / Molecular biology of steroid hormone synthesis. by Miller (1988)
10.1146/annurev.ph.50.030188.002235 / Annu Rev Physiol / Regulation of the synthesis of steroidogenic enzymes in adrenal cortical cells by ACTH. by Simpson (1988)
10.1146/annurev.ge.23.120189.002103 / Annu Rev Genet / The molecular genetics of 21-hydroxylase deficiency. by Miller (1989)
{'key': '2019041122575340600_R5'}
10.1210/jcem.86.8.7748 / J Clin Endocrinol Metab / Heterozygous mutation in the cholesterol side chain cleavage enzyme (p450scc) gene in a patient with 46,XY sex reversal and adrenal insufficiency. by Tajima (2001)
10.1210/endo.131.1.1611996 / Endocrinology / Inherited congenital adrenal hyperplasia in the rabbit: absent cholesterol side-chain cleavage cytochrome P450 gene expression. by Pang (1992)
10.1016/S1569-2558(08)60344-6 / Advances in molecular and cell biology. / Reactions carried out by P450c21 and P450c17. by Chung (1996)
10.1210/endo.140.12.7177 / Endocrinology / Tissue-specific, hormonal and developmental regulation of CYP11A1/LacZ expression in transgenic mice leads to adrenocortical zone characterization. by Hu (1999)
10.1210/endo.132.5.7682938 / Endocrinology / Inherited congenital adrenal hyperplasia in the rabbit is caused by a deletion in the gene encoding cytochrome P450 cholesterol side-chain cleavage enzyme. by Yang (1993)
{'key': '2019041122575340600_R11', 'first-page': '1', 'article-title': 'Development of male accessory glands.', 'author': 'Cunha', 'year': '1979', 'journal-title': 'Accessory glands of the male reproductive tract.'} / Accessory glands of the male reproductive tract. / Development of male accessory glands. by Cunha (1979)
10.1056/NEJM199202273260906 / N Engl J Med / Androgen resistance–the clinical and molecular spectrum. by Griffin (1992)
10.1172/JCI106966 / J Clin Invest / Studies on the pathogenesis of the pseudohermaphroditism in the mouse with testicular feminization. by Goldstein (1972)
10.1073/pnas.95.16.9424 / Proc Natl Acad Sci USA / Mineralocorticoid receptor knockout mice: pathophysiology of Na+ metabolism. by Berger (1998)
10.1101/gad.9.13.1608 / Genes Dev / Targeted disruption of the glucocorticoid receptor gene blocks adrenergic chromaffin cell development and severely retards lung maturation. by Cole (1995)
10.1016/S0896-6273(00)80491-2 / Neuron / Corticotropin releasing factor receptor 1-deficient mice display decreased anxiety, impaired stress response, and aberrant neuroendocrine development. by Smith (1998)
10.1056/NEJM199612193352503 / N Engl J Med / The pathophysiology and genetics of congenital lipoid adrenal hyperplasia. International Congenital Lipoid Adrenal Hyperplasia Consortium. by Bose (1996)
{'key': '2019041122575340600_R18', 'first-page': '221', 'article-title': 'Regulation of the acute production of steroids in steroidogenic cells.', 'volume': '17', 'author': 'Stocco', 'year': '1996', 'journal-title': 'Endocr Rev'} / Endocr Rev / Regulation of the acute production of steroids in steroidogenic cells. by Stocco (1996)
10.1073/pnas.94.21.11540 / Proc Natl Acad Sci USA / Targeted disruption of the mouse gene encoding steroidogenic acute regulatory protein provides insights into congenital lipoid adrenal hyperplasia. by Caron (1997)
10.1210/jcem-69-6-1148 / J Clin Endocrinol Metab / Molecular characterization of a Leydig cell tumor presenting as congenital adrenal hyperplasia. by Solish (1989)
10.1210/mend-4-6-893 / Mol Endocrinol / Expression of human 21-hydroxylase (P450c21) in bacterial and mammalian cells: a system to characterize normal and mutant enzymes. by Hu (1990)
10.1042/bj2740813 / Biochem J / Regulated expression of cytochrome P-450 scc (cholesterol-side-chain cleavage enzyme) in cultured cell lines detected by antibody against bacterially expressed human protein. by Hu (1991)
10.1006/dbio.2000.0129 / Dev Biol / Two sox9 genes on duplicated zebrafish chromosomes: expression of similar transcription activators in distinct sites. by Chiang (2001)
10.1073/pnas.83.24.9601 / Proc Natl Acad Sci USA / Nucleotide sequence analysis of murine 21-hydroxylase genes: mutations affecting gene expression. by Chaplin (1986)

Dates

Type	When
Created	22 years, 11 months ago (Oct. 1, 2002, 2:03 p.m.)
Deposited	6 years, 4 months ago (April 12, 2019, 9:55 a.m.)
Indexed	1 week ago (Aug. 30, 2025, 1:19 p.m.)
Issued	23 years, 1 month ago (Aug. 1, 2002)
Published	23 years, 1 month ago (Aug. 1, 2002)
Published Print	23 years, 1 month ago (Aug. 1, 2002)

Funders 0

None

BibTeX

@article{Hu_2002, title={Steroid Deficiency Syndromes in Mice with Targeted Disruption of Cyp11a1}, volume={16}, ISSN={1944-9917}, url={http://dx.doi.org/10.1210/me.2002-0055}, DOI={10.1210/me.2002-0055}, number={8}, journal={Molecular Endocrinology}, publisher={The Endocrine Society}, author={Hu, Meng-Chun and Hsu, Nai-Chi and El Hadj, Noomen Ben and Pai, Chin-I and Chu, Hsueh-Ping and Wang, Chi-Kuang Leo and Chung, Bon-chu}, year={2002}, month=aug, pages={1943–1950} }

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