DOI: 10.1172/jci33355. Correction of ClC-1 splicing eliminates chloride channelopathy and myotonia in mouse models of myotonic dystrophy

Correction of ClC-1 splicing eliminates chloride channelopathy and myotonia in mouse models of myotonic dystrophy

10.1172/jci33355

Crossref journal-article

American Society for Clinical Investigation

Journal of Clinical Investigation (232)

Bibliography

Wheeler, T. M., Lueck, J. D., Swanson, M. S., Dirksen, R. T., & Thornton, C. A. (2007). Correction of ClC-1 splicing eliminates chloride channelopathy and myotonia in mouse models of myotonic dystrophy. Journal of Clinical Investigation.

Authors 5

Thurman M. Wheeler (first)
John D. Lueck (additional)
Maurice S. Swanson (additional)
Robert T. Dirksen (additional)
Charles A. Thornton (additional)

References 31 Referenced 41

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10.1212/01.WNL.0000148482.40683.88 / Neurology. by Berg (2004)
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10.1113/jphysiol.1990.sp018110 / J. Physiol. by Franke (1990)
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10.1152/ajpcell.00336.2006 / Am. J. Physiol. Cell Physiol. by Lueck (2007)
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Trip, J., Drost, G., van Engelen, B.G., and Faber, C.G. 2006. Drug treatment for myotonia. Cochrane Database Syst. Rev. CD004762. (10.1002/14651858.CD004762.pub2)
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10.1007/BF00656997 / Pflugers Arch. by Hamill (1981)

Dates

Type	When
Created	17 years, 9 months ago (Nov. 15, 2007, 8:18 p.m.)
Deposited	2 years, 1 month ago (Aug. 3, 2023, 12:19 p.m.)
Indexed	3 weeks, 3 days ago (Aug. 12, 2025, 6:09 p.m.)
Issued	17 years, 9 months ago (Nov. 15, 2007)
Published	17 years, 9 months ago (Nov. 15, 2007)
Published Online	17 years, 9 months ago (Nov. 15, 2007)

Funders 0

None

BibTeX

@article{Wheeler_2007, title={Correction of ClC-1 splicing eliminates chloride channelopathy and myotonia in mouse models of myotonic dystrophy}, ISSN={0021-9738}, url={http://dx.doi.org/10.1172/jci33355}, DOI={10.1172/jci33355}, journal={Journal of Clinical Investigation}, publisher={American Society for Clinical Investigation}, author={Wheeler, Thurman M. and Lueck, John D. and Swanson, Maurice S. and Dirksen, Robert T. and Thornton, Charles A.}, year={2007}, month=nov }

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