DOI: 10.1172/jci113064. Altered kinetic properties of the branched-chain alpha-keto acid dehydrogenase complex due to mutation of the beta-subunit of the branched-chain alpha-keto acid decarboxylase (E1) component in lymphoblastoid cells derived from patients with maple syrup urine disease.

Altered kinetic properties of the branched-chain alpha-keto acid dehydrogenase complex due to mutation of the beta-subunit of the branched-chain alpha-keto acid decarboxylase (E1) component in lymphoblastoid cells derived from patients with maple syrup urine disease.

10.1172/jci113064

Crossref journal-article

American Society for Clinical Investigation

Journal of Clinical Investigation (232)

Bibliography

Indo, Y., Kitano, A., Endo, F., Akaboshi, I., & Matsuda, I. (1987). Altered kinetic properties of the branched-chain alpha-keto acid dehydrogenase complex due to mutation of the beta-subunit of the branched-chain alpha-keto acid decarboxylase (E1) component in lymphoblastoid cells derived from patients with maple syrup urine disease. Journal of Clinical Investigation, 80(1), 63â70.

Authors 5

Y Indo (first)
A Kitano (additional)
F Endo (additional)
I Akaboshi (additional)
I Matsuda (additional)

References 0 Referenced 40

None

Dates

Type	When
Created	17 years, 6 months ago (Feb. 28, 2008, 3:28 p.m.)
Deposited	2 years, 1 month ago (Aug. 3, 2023, 12:55 p.m.)
Indexed	3 months, 1 week ago (May 29, 2025, 12:05 p.m.)
Issued	38 years, 2 months ago (July 1, 1987)
Published	38 years, 2 months ago (July 1, 1987)
Published Print	38 years, 2 months ago (July 1, 1987)

Funders 0

None

BibTeX

@article{Indo_1987, title={Altered kinetic properties of the branched-chain alpha-keto acid dehydrogenase complex due to mutation of the beta-subunit of the branched-chain alpha-keto acid decarboxylase (E1) component in lymphoblastoid cells derived from patients with maple syrup urine disease.}, volume={80}, ISSN={0021-9738}, url={http://dx.doi.org/10.1172/jci113064}, DOI={10.1172/jci113064}, number={1}, journal={Journal of Clinical Investigation}, publisher={American Society for Clinical Investigation}, author={Indo, Y and Kitano, A and Endo, F and Akaboshi, I and Matsuda, I}, year={1987}, month=jul, pages={63–70} }

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