DOI: 10.1016/s0969-2126(00)00105-2. Crystal structure of human branched-chain α-ketoacid dehydrogenase and the molecular basis of multienzyme complex deficiency in maple syrup urine disease

Crystal structure of human branched-chain α-ketoacid dehydrogenase and the molecular basis of multienzyme complex deficiency in maple syrup urine disease

10.1016/s0969-2126(00)00105-2

Crossref journal-article

Elsevier BV

Structure (78)

Bibliography

Ãvarsson, A., Chuang, J. L., Max Wynn, R., Turley, S., Chuang, D. T., & Hol, W. G. (2000). Crystal structure of human branched-chain Î±-ketoacid dehydrogenase and the molecular basis of multienzyme complex deficiency in maple syrup urine disease. Structure, 8(3), 277â291.

Authors 6

Arnthor Ævarsson (first)
Jacinta L Chuang (additional)
R Max Wynn (additional)
Stewart Turley (additional)
David T Chuang (additional)
Wim GJ Hol (additional)

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Dates

Type	When
Created	23 years, 1 month ago (July 25, 2002, 9:54 a.m.)
Deposited	2 years, 4 months ago (April 8, 2023, 6:48 p.m.)
Indexed	30 minutes ago (Aug. 29, 2025, 9:27 p.m.)
Issued	25 years, 5 months ago (March 1, 2000)
Published	25 years, 5 months ago (March 1, 2000)
Published Print	25 years, 5 months ago (March 1, 2000)

Funders 0

None

BibTeX

@article{_varsson_2000, title={Crystal structure of human branched-chain α-ketoacid dehydrogenase and the molecular basis of multienzyme complex deficiency in maple syrup urine disease}, volume={8}, ISSN={0969-2126}, url={http://dx.doi.org/10.1016/s0969-2126(00)00105-2}, DOI={10.1016/s0969-2126(00)00105-2}, number={3}, journal={Structure}, publisher={Elsevier BV}, author={Ævarsson, Arnthor and Chuang, Jacinta L and Max Wynn, R and Turley, Stewart and Chuang, David T and Hol, Wim GJ}, year={2000}, month=mar, pages={277–291} }

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